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目的探讨髌骨软骨母细胞瘤(CB)的临床特点、病理形态、免疫表型、影像学及预后。方法报告1例髌骨软骨母细胞瘤,复习近38年国内外有关文献报道,分析髌CB瘤的临床、病理和影像的诊断与鉴别诊断及预后资料。结果患者男性,21岁。左膝部疼痛伴左下肢无力半年。X线片可见髌骨内溶骨性破坏。镜下肿瘤由圆形或多角形软骨母细胞、多核巨细胞、局灶样类软骨组织及小的钙化灶等成分组成,瘤组织S-100(+)。结论软骨母细胞瘤发生在髌骨甚为罕见,其发生率约占软骨母细胞瘤的2%,因其在组织学上表现的多样性应临床、病理学、影像学检查三结合进行诊断。
Objective To investigate the clinical features, pathological morphology, immunophenotype, imaging and prognosis of patella chondroblastoma (CB). Methods One case of patella chondroblastoma was reported and reviewed in the literature for nearly 38 years at home and abroad. The diagnosis, differential diagnosis and prognosis of patella CB were analyzed. Results The patient was male, 21 years old. Left knee pain with left leg weakness for six months. X-ray shows patella osteolytic destruction. Microscopic tumor by round or polygonal cartilage cells, multinucleated giant cells, focal like cartilage tissue and small calcification and other components, tumor tissue S-100 (+). Conclusion The occurrence of chondroblastoma in the patella is very rare. The incidence of chondroblastoma is about 2% of that of chondroblastoma. Because of its diversity in histology, it should be combined with clinical, pathological and imaging examinations.