Aldrich氏综合征又名Wiskott-Aldrich氏综合征,其特点为血小板减少性紫斑,湿疹样皮疹及重复发作的感染,本综合征为遗传性疾病,男性患病,女性遗传,其遗传方式为性连锁隐性遗传,恰似血友病,但尚有少数病例未发现家族史。起病多自生后第一个月开始,便血最为常见,预后险恶,或由出血死亡,或由感染死亡。 1954年Aldrich氏等首先报告本综合征 Aldrich’s syndrome, also known as Wiskott-Aldrich’s syndrome, is characterized by thrombocytopenic purpura, eczematous rash and recurrent infections. The syndrome is a hereditary disease, male disease, and female inheritance, with a genetic pattern of sex Hidden recessive chain, like hemophilia, but there are still a few cases did not find a family history. The first month after the onset of multiple spontaneous start, the most common blood in the stool, the prognosis sinister, or died of bleeding, or by infection. 1954 Aldrich’s first report of this syndrome