成人先天性丙种球蛋白缺乏症较少见,伴有类风湿性关节炎的更为罕见。国内尚未见报道,我院收治1例,介绍如下。病历摘要男,24岁,住院号227351。患者自2～3岁起反复发作支气管肺炎和皮肤等处感染。多次住院,经用抗生素,注射丙种球蛋白感染控制。多次查丙种球蛋白均显著减少。1982年2月出现双手近端指间关节及 Adult congenital gamma globulin deficiency is less common, more common with rheumatoid arthritis. Not yet reported in our country, admitted to our hospital in 1 case, described below. Medical summary Male, 24 years old, hospital number 227351. Patients from 2 to 3 years old recurrent bronchial pneumonia and skin infections. Repeated hospitalization, the use of antibiotics, injection of gamma globulin infection control. Check gamma globulin were significantly reduced. 1982 February hands proximal interphalangeal joint and