本文分析了苏联医学科学院神经病学研究所诊查的400例肌萎缩测束硬化症,其中有一半以上经过了3—5次的诊查。258人是男性,占大多数。226人是在劳动能力最强的年龄(50岁之前)患病,其中102人在40岁以前,17人在30以前。不论哪一类型,男性占多数,但延髓型是个例外,100人中有65人是女性,几乎比男性多2倍。最长病程达12年,但8、10、12年者只占少数。 This article analyzes 400 cases of amyotrophic sclerosis diagnosed by the Institute of Neurology of the Soviet Academy of Medical Sciences. More than half of them were examined 3-5 times. 258 are men, accounting for the majority. Of the 226 people who were ill at the age of most able (50 years old), 102 were 40 years old and 17 were 30. Regardless of the type, men make up the majority, with the exception of the bulbar type, where 65 out of 100 are women, almost 2 times more likely than men. The longest duration of up to 12 years, but 8,10,12 years accounted for only a minority.