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家族性非溶血性黄疸系一种罕见的家族遗传体质性疾病,可能系肝细胞排泄胆红素的功能发生障碍所致。临床上以疲乏、轻度黄疸、血清间接胆红素增加为其特征。其预后良好。吉尔勃特(Gilbert)氏远在50余年前(1902)首先报告此病,故(?)称为吉尔勃特氏病;以后文献采用之名称有:“生理性胆血症”,“家族性非溶血性黄疸”,“单纯性家族性胆血症”,“体质性肝机能不良”,“青年性慢性肝炎”,“间歇性幼年性黄疸”,“遗传性非溶血性胆红素血症”及“体质性血清胆红素过多症”等。輓近外国文献采用“体质性肝机能不良”作病名者较多。
Familial non-hemolytic jaundice is a rare familial hereditary disease that may be due to dysfunction of the excretion of bilirubin by hepatocytes. Clinically, fatigue, mild jaundice, increased serum indirect bilirubin as its characteristics. Its prognosis is good. Gilbert’s disease was first reported more than 50 years ago (1902), so (?) Is called Gilbert’s disease; later references used were: “physiological cholestasis”, “familial Non-hemolytic jaundice, ”“ simple familial cholecystitis, ”“ constitutional liver dysfunction, ”“ chronic hepatitis with juvenile age, ”“ intermittent juvenile jaundice, ”“ hereditary nonhemolytic bilirubin ”And“ excessive serum bilirubin syndrome ”and so on. Close to foreign literature using “constitutional liver dysfunction” as disease name more.