软骨肉瘤是起源于软骨细胞或间胚叶组织的一种少见的恶性肿瘤,好发于四肢长骨、骨盆、肋骨及上肢腕骨等处。头颈部少见,约占全身软骨肉瘤的10%,多发生于鼻腔及上颌窦,其他鼻窦少见。由于软骨肉瘤的生物学行为个体之间差异较大,加之鼻腔鼻窦解剖复杂、部位隐蔽,其临床病理特征亦 Chondrosarcoma is a rare malignant tumor that originates from chondrocytes or mesoderm. It occurs in long bones, pelvis, ribs and upper extremity carpal bones. Head and neck rare, accounting for about 10% of systemic chondrosarcoma, occurred in the nasal cavity and maxillary sinus, rare other sinus. Because of the biological behavior of chondrosarcoma large differences between individuals, combined with nasal sinus anatomy complex, hidden parts, the clinical and pathological features are also