腺泡状软组织肉瘤(ASPS)是一种罕见的肿瘤,大多发生在青年人,以四肢软组织好发。ASPS组织学特征是肿瘤细胞被纤维血管分隔成巢状或器官样结构。当ASPS发生于少见部位时诊断较为困难,需与一些常见的肿瘤,如颗粒细胞瘤、副神经节瘤、透明细胞肉瘤,转移性肾透明细胞癌 Acinar soft tissue sarcoma (ASPS) is a rare tumor, mostly in young people, with soft tissue limbs hair. Histological features of ASPS are that tumor cells are separated by fibroids into nests or organ-like structures. When ASPS occurs more often than not, it is difficult to diagnose it. Some common tumors such as granulosa cell tumor, paraganglioma, clear cell sarcoma, metastatic renal clear cell carcinoma