布-加综合征(BCS)在西方国家多指Chiari病,即主肝静脉(MHVs)阻塞,以血栓形成多见。在我国等亚洲国家出现的下腔静脉膜性梗阻(MOVC),其表现类似Chiari病。因此,我们目前认为广义的BCS是指MHVs出口部和/或肝后段下腔静脉血流受阻所引起的肝后性门静脉高压和/或下腔静脉高压综合征 Budd-Chiari syndrome (BCS) in Western countries, mostly refers to Chiari disease, the main hepatic vein (MHVs) obstruction, thrombosis more common. In China and other Asian countries appear inferior vena cava obstruction (MOVC), its performance is similar to Chiari disease. Therefore, we now consider the broad term BCS to mean posterior hepatic portal hypertension and / or inferior vena cava hypertension caused by blocked flow of the inferior vena cava of the MHVs and / or the posterior segment of the liver