主动脉瓣二叶式畸形是常见的先天性心脏畸形,但其临床症状多不典型,早期不易发现,仅凭临床诊断常误诊为风湿性心脏瓣膜病等其他心脏病;应用超声心动图能迅速、准确地对主动脉瓣二叶式畸形做出诊断,而且能够发现其易并存主动脉瓣狭窄、主动脉瓣关闭不全、升主动脉扩张、室间隔缺损等合并症。本文对近年来在我院就诊的36例先天性二叶式主动脉瓣畸形患者的的超声特点进行回顾性分析,现报告如 Aortic valve deformity is a common congenital heart disease, but its clinical symptoms are atypical, not easy to find early, clinical diagnosis often misdiagnosed as rheumatic heart valve disease and other heart disease; application of echocardiography can quickly , Accurate diagnosis of aortic valve bilobectomy, but also to find its easy to coexist aortic stenosis, aortic insufficiency, ascending aortic dilatation, ventricular septal defect and other complications. In this paper, 36 cases of congenital bicuspid aortic valve malformations in our hospital in recent years were retrospectively analyzed.