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患者36岁,因不规则阴道流血于1995年2月8日入院。既往月经规律,经期5~7天,经量正常。3个月前无明显原因出现阴道流血,淋漓不断,量少,无恶心呕吐,不伴有腹痛及发热,曾用药物治疗(药物不详)效果不佳。入院查体:T36.8℃,P76次/min,R18次/min,Bp14/10kPa。妇科检查:外阴经产式,阴道壁光滑,宫颈5~7点处有一3.0cm×3.Ocm暗红色肿物,表面轻度糜烂渗血、质软、无蒂。子宫平位,正常大小,双附件区未触及包块。宫颈肿物活检报告为腺泡状软组织肉瘤。即在硬膜外麻醉下行次广泛全子宫切除术。予以单一环磷酰胺化疗一个疗程后出院。随访18个月,未发现有转移病灶。 讨论:腺泡状软组织肉瘤多见于青年女性,好发于深部肌肉组织或肌肉筋膜处,发生于宫颈部位者罕见。临床上,常表现为深部软组织的无痛性肿块,生长缓慢,预后较好,有长达20年病史者。本病主要是血行转移,转移率达50%,常转移至肺、脑和骨
The patient, 36, was admitted to hospital on February 8, 1995 due to irregular vaginal bleeding. Previous menstrual regularity, menstrual 5-7 days, the amount of normal. 3 months ago, there is no obvious reason vaginal bleeding, dripping, less, no nausea and vomiting, without abdominal pain and fever, once medication (drug unknown) ineffective. Admission examination: T36.8 ℃, P76 times / min, R18 times / min, Bp14 / 10kPa. Gynecological examination: genital production, vaginal wall smooth, cervix 5 to 7 at a 3.0cm × 3.Ocm dark red tumor, the surface of mild erosion bleeding, soft, pedicle. Flat uterus, normal size, double annex area did not touch the mass. Cervical biopsy was reported as alveolar soft tissue sarcoma. That epidural anesthesia underwent extensive hysterectomy. To a single cyclophosphamide chemotherapy after a discharge. Follow-up 18 months, no metastatic lesions were found. Discussion: Acinar soft tissue sarcoma more common in young women, occur in deep muscle or muscle fascia, occurred in the cervix are rare. Clinically, often manifested as painless mass of deep soft tissue, slow growth, the prognosis is good, up to 20 years of history. The disease is mainly blood metastasis, the transfer rate of 50%, often transferred to the lungs, brain and bone