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患儿,男,6岁。因咳嗽2周,发烧一周,双手、鼻尖、耳廓发绀4天。当地经青霉素治疗无效,在采血出现血出即凝现象体检:T:38℃,两肺闻及湿罗音以中下为著,双手、鼻尖、耳廓见发绀,花斑状。先后暴露双足和双下肢5分钟后皮肤发生同样的紫绀现象,采血时血出即凝。但局部经保暖后紫绀消失,颜色恢复正常,采血顺利。血常规和血小板均正常,肝、肾功能正常。胸片:两肺门阴影增浓,两下肺纹理增多,并见小片状阴
Children, male, 6 years old. Due to cough 2 weeks, fever a week, hands, nose, auricle cyanosis 4 days. Local penicillin treatment ineffective blood in the blood that is coagulation phenomenon Physical examination: T: 38 ℃, both lungs and wet rales to the middle of the pair, hands, nose, ears see cyanosis, piebald-like. Has exposed both feet and lower extremities 5 minutes after the same cyanosis of the skin, blood when blood coagulation. However, after partial warm cyanosis disappeared, the color returned to normal, blood collection smoothly. Blood and platelets are normal, liver and kidney function is normal. Chest X-ray: Shadow of the two hives thickening, increased lungs under the two, and see a small piece of shade