先天性孤立性镫骨上结构固定罕见 ,该文报告首例先天性镫骨单足与鼓岬的固定。患者男性 ,4 2岁。主诉右耳非进行性听力减退多年 ,左耳听力正常 ,无头颅外伤或慢性中耳炎史 ,无耳鸣、眩晕 ,无耳手术及家族性耳聋史。检查发现 :外耳及鼓膜正常 ,512 Hz音叉检查任内试验右耳阴性 , Congenital solitary ossicular structure fixed rare, the article reports the first case of congenital tarsal foot and promontory promontory fixed. Male patient, 4 2 years old. The main complaint of right ear non-progressive hearing loss for many years, left ear hearing normal, no head trauma or chronic otitis media history, no tinnitus, dizziness, no ear surgery and familial deafness history. Examination found that: the outer ear and tympanic membrane normal, 512Hz tuning fork test any test negative ear,