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结节性硬化症合并肾血管平滑肌脂肪瘤,肾透明细胞癌是较为罕见病例,现把我们的一例报道于下: 男性,30岁。1981年2月5日因发热、消瘦、乏力就诊,超声发现“右上腹包块”。体验:贫血,体温38℃。鼻翼两侧有融合成片的疣状结节,呈蝶形分布。颞、枕部、阴囊部有散在大小不等的瘤样肿物。肘膝以下密布无色素斑,趾甲内侧有一赘生物。肋缘下触及一肿块与肝脏分界不清,表面光滑。实验室检查:血红蛋白6.5克%,红细胞234万/立方毫米,白细胞9,600/立方毫米,血沉125毫米,碱性磷酸酶10单位,肝、肾功能在正常范围,超声提示囊性肿物来自肝脏。钡剂检查:胃十二指肠被压至左上
Tuberous sclerosis with renal angiomyolipoma, renal clear cell carcinoma is a relatively rare case, and our case is reported below: Male, 30 years old. On February 5, 1981, due to fever, weight loss, and fatigue, he was diagnosed as having a “right upper abdominal mass.” Experience: Anemia, body temperature 38 °C. There are braided nodules that fuse into a patch on both sides of the nose and are butterfly-shaped. Sputum, occipital, and scrotum are scattered tumors of different sizes. There were no pigmented spots under the elbow and knees, and there was a living creature inside the toenail. Under the costal margin, a mass and liver are unclear and the surface is smooth. Laboratory tests: Hemoglobin 6.5g%, RBC 2.34 million/mm 3, WBC 9,600/mm 3, ESR 125mm, Alkaline phosphatase 10 units, Liver, kidney function in the normal range, ultrasound prompted cystic mass from the liver. Liniment check: stomach and duodenum are pressed to the upper left