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患者女,14岁。右眼失明10年,右眼球突出和阵发性痛6年余。查体发现眼球下方深部包块。眼底检查:双侧视盘边界不清,色苍白,有新生血管,高起约3D,静脉略纡曲扩张。右眼球明显突出。眼科诊断为右眶内肿瘤,随即入院行眶内肿瘤切除术。手术中发现肿瘤位于眶尖部,与视神经关系紧密,但与颅内无沟通。术后1年,患者出现头痛、呕吐等颅内压增高症状,CT示左侧脑室及三脑室内肿瘤而再次入院。行开颅手术切除,术后出现脑积水行侧脑室静脉分流术好转出院。术后3年再度出现颅内压增高症状。经CT发现右侧脑室内肿瘤并侵及颞叶
Female patient, 14 years old. Right eye blindness 10 years, right eyeballs and paroxysmal pain more than 6 years. Examination found that the bottom of the mass of deep mass. Fundus examination: bilateral optic disc border is unclear, pale, with new blood vessels, high starting from about 3D, venous slightly distorted expansion. The right eye is clearly prominent. Ophthalmology diagnosis of right orbital tumor, then admitted to the hospital orbital tumor resection. Surgical found tumor located in the orbital apex, closely related with the optic nerve, but no communication with the brain. One year after surgery, the patient developed symptoms of increased intracranial pressure, such as headache and vomiting. CT showed left ventricle and three-ventricle tumors and was re-admitted. Line craniotomy resection, hydrocephalus after lateral ventricle shunt improved discharge. 3 years after the recurrence of increased intracranial pressure symptoms. The right cerebral ventricle tumor was found by CT and invaded the temporal lobe