颞骨胆脂瘤分为先天性胆脂瘤和后天性胆脂瘤,其本质都是角化复层鳞状上皮在一个完全封闭或相对封闭的解剖部位不断增殖、分化,上皮脱屑不断堆积而又不能排空所致。颞骨先天性胆脂瘤约占总个胆脂瘤的2%,常易被临床医师忽视引起误诊。本文就其病因、病理、临床表现、影像诊断与鉴 Temporal bone cholesteatoma is divided into congenital cholesteatoma and acquired cholesteatoma, which in essence are keratinized stratified squamous epithelium in a completely closed or relatively closed dissection continue to proliferate, differentiation, epithelial scaling continue to accumulate Can not be emptied again. Temporal bone congenital cholesteatoma accounted for about 2% of the total cholesteatoma, often easily ignored by clinicians cause misdiagnosis. This article on its etiology, pathology, clinical manifestations, imaging diagnosis and Kam