To the Editor:We described a successful treatment of a case diagnosed with arrhythmogenic right ventricular cardiomyopathy (ARVC) with absent pulmonary valve (APV).rnA 10?year?old male child was referred to our emergency room for acute right heart failure who had two times of syncope before. On admission, the electrocardiogram showed that T?wave inversions were visible in most leads, QRS duration was prolonged with 120 ms, and the terminal depolarizations might be interpreted as epsilon waves in leads V1–V5 [Figure 1a arrows]. Transthoracic echocardiography and computed tomography scan were performed;the right ventricle chamber seemed larger than the left ventricle chamber [Figure 1b], with APV, atrial septal defect, and moderate tricuspid regurgitation.