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目的探讨永存左上腔静脉与胎儿心脏畸形,尤其是主动脉缩窄及发育不良之间的关系。方法回顾性分析4 664例胎儿超声心动图结果 ,计算左上腔静脉和先天性心脏畸形的比值比(OR值)与左上腔静脉和先天性主动脉缩窄及发育不良的比值比等。结果 4 664胎儿超声心动图结果中,无结构性胎儿心脏畸形4 004例,合并左上腔静脉(LSVC)38例(0.95%);结构性心脏畸形660例,合并LSVC 62例(9.39%)(OR=10.8)。660例心脏畸形中,主动脉缩窄和主动脉发育不良47例,同时合并LSVC 17例(36.17%)(OR=7.15)。结论胎儿永存左上腔静脉同样提示胎儿结构性心脏畸形的危险性明显增加。并且胎儿患主动脉缩窄及发育不良的可能性亦增加。提示如果发现LSVC,应追踪观察,除外先天性心脏畸形,尤其是主动脉缩窄及发育不良。
Objective To investigate the relationship between periventricular left superior vena cava and fetal heart malformation, especially aortic constriction and dysplasia. Methods The results of 4 664 fetal echocardiographic studies were retrospectively analyzed. The odds ratio (OR) between the left superior vena cava and congenital heart disease and the ratio between the left superior vena cava and congenital aortic constriction and dysplasia were calculated. RESULTS: Among 4 664 fetuses, there were 4 004 cases of uncorcompanied fetal cardiac malformations, 38 cases (0.95%) with left superior vena cava (LSVC), 660 cases of structural heart malformations, 62 cases (9.39%) with LSVC OR = 10.8). Of the 660 patients with cardiac abnormalities, 47 had aortic constriction and aortic dysplasia, and 17 had LSVC (36.17%) (OR = 7.15). Conclusions Fetal perpetuated left superior vena cava also suggests a significant increase in the risk of fetal structural heart malformations. And the possibility of fetal narrowing of the aorta and dysplasia also increased. Tip If LSVC is found, follow-up should be followed, except for congenital heart defects, especially aortic constriction and hypoplasia.