心内膜弹力纤维增生症(EFE)为小儿原发性心肌病中的一种类型,其特征性的病理改变以左心室受累为主,我们发现一例以右心病变为主的EFE,较为罕见,今报告如下: Endocardial fibroelastosis (EFE) is a type of primary cardiomyopathy in children and its characteristic pathological changes are mainly left ventricular involvement. We found that one case of right heart lesion-based EFE was relatively rare This report is as follows: