通过介绍一例先天性动眼神经麻痹合并眼睑及瞳孔周期性痉挛弛缓患儿，对该病的名称、临床特征、发病机理、诊断与鉴别诊断及治疗等方面进行了讨论，为人们认识和探讨周期痉挛性动眼神经麻痹这种有趣而又罕见的眼疾提供了证据。 By introducing a case of congenital oculomotor paralysis with eyelid and pupillary spasm in children with relaxation, the name of the disease, clinical features, pathogenesis, diagnosis and differential diagnosis and treatment were discussed, for people to understand and explore the cycle Spasmodic oculomotor palsy is an interesting and rare eye disease that provides evidence.