论文部分内容阅读
滑膜软骨肉瘤(synovial chondrosarcoma,SCS)是一种软骨性恶性肿瘤,极其罕见,可原发或继发于滑膜软骨瘤病。源于颞下颌关节(temporomandibular joint,TMJ)的SCS仅见3例报道。本文报告1例罕见的累及颞下间隙且破坏颅底的TMJ-SCS,手术利用数字导板确定肿瘤边界并将其切除,同期用髂骨瓣修复颅底、带蒂锁骨瓣重建髁突和颞深筋膜脂肪瓣作为骨组织间置物。术后随访1 a,患者面型对称,开口度22 mm;影像学检查显示局部无复发和骨转移,但出现肺转移。
Synovial chondrosarcoma (SCS) is a cartilage malignancy that is extremely rare and can be primary or secondary to synovial chondromatosis. Only three cases of SCS originated from temporomandibular joint (TMJ) were reported. In this paper, we report a rare case of TMJ-SCS involving the infratemporal space and destroying the base of the skull. A digital guide was used to determine the tumor boundary and resect the tumor. The iliac flap was used to repair the skull base and the pedicle clavicular flap to reconstruct the condyles and temporal Fascia fat flap as bone tissue compartment. After a follow-up of 1 year, the patient was symmetrical in shape and the opening was 22 mm. Radiographic examination showed no local recurrence and bone metastasis but pulmonary metastasis.