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作者报告一例后天性伴有肺泡壁纤维化和纵隔淋巴结肿大的低γ-球蛋白血症,经静脉输入γ-球蛋白,得到了即时的和良好的效果。患者系一34岁妊妇,患肺部感染,合并双侧膝关节积水和肝脾肿大。胸部X线表现为两肺下野呈粟粒样病变伴有弥漫性肺实质炎,右纵隔淋巴结肿大。肺活组织检查发现肺气肿病变伴有肺泡壁纤维化,细枝气管正常。肺功能检查提示混合性通气功能障碍,以弥散功能障碍最明显。一氧化碳弥散绝对值降低50%。
The authors report a case of acquired hypogammaglobulinemia with acquired alveolar wall fibrosis and mediastinal lymph nodes acquired by intravenous administration of γ-globulin, resulting in immediate and good results. The patient is a 34-year-old pregnant woman suffering from pulmonary infection, bilateral knee joint water and hepatosplenomegaly. Chest X-ray showed two lung mites-like lesions associated with diffuse pulmonary pituitary disease, right mediastinal lymph nodes. Lung biopsy found that emphysematous lesions associated with alveolar wall fibrosis, thin branches and trachea normal. Pulmonary function tests suggest mixed ventilatory dysfunction in order to diffuse dysfunction most obvious. The absolute value of carbon monoxide dispersion is reduced by 50%.