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进行性系统性硬化症伴弥漫性硬皮病者的尸检中,心肌纤维化常见,占12~81%,其发病机制尚有争论。本文应用运动试验和放射性核素技术,研究本病患者的心肺功能,以探讨心脏受累的病理生理情况。方法:26例有手指、手、前臂和躯干皮肤增厚,符合美国风湿病学会关于系统性硬化症诊断标准的患者,先进行极量活动平板试验,以 ST 段压低≥1毫米为异常。运动高峰前1分钟,静脉注射~(201)铊2.0毫居里,在运动后5分钟及3小时取前位、45°及70°
In patients with progressive systemic sclerosis and diffuse scleroderma autopsy, myocardial fibrosis is common, accounting for 12 ~ 81%, the pathogenesis is still controversial. In this paper, exercise tests and radionuclide techniques to study the cardiopulmonary function of patients with this disease to explore the pathophysiology of cardiac involvement. Methods: Twenty - six patients with thickening of the skin of fingers, hands, forearms and torso, in line with the American College of Rheumatology criteria for the diagnosis of systemic sclerosis, first carried out an extremely flat activity test to ST segment depression ≥ 1 mm as an exception. 1 minute before exercise peak, intravenous ~ (201) thallium 2.0 millicuries, 5 minutes after exercise and 3 hours to take the first bit, 45 ° and 70 °