阵发性睡眠性血红蛋白尿症(简称PNH)是一种少见的慢性溶血性贫血,易发生血栓,现将我科收治的一例报告如下: 患者滕××,男、3O岁。于1990年8月11日入院。患者于10年前发现工作劳累后出现酱油色尿,多在夜间及晨起时发生,严重时白天也可出现,每年可出现10余次,每次持续2～3天,伴有乏力、头晕。五年前出现皮肤发黄。今年来不定时发烧。3天来觉头晕、头痛、伴言语不清,右眼视物不清,右上、下肢活动不灵。查体;贫血貌、全身皮肤及巩膜黄染。心肺听诊无异常,肝脾不大。瞳孔等大。视野:右鼻侧、左颞侧呈不规则暗点缺损。右侧鼻唇沟稍浅,口角稍向左歪斜,伸舌稍向右偏,皱额闭目正常。右侧上、下肢肌 Paroxysmal nocturnal hemoglobinuria (referred to as PNH) is a rare chronic hemolytic anemia, thrombosis prone, now we receive a case report as follows: Patients Teng × ×, male, 3O years old. Admitted to hospital on August 11, 1990. 10 years ago, the patient found after work tired soy sauce color urine, mostly at night and early morning when the occurrence of severe daytime may occur more than 10 times each year, each lasting 2 to 3 days, accompanied by fatigue, dizziness . The skin yellowed five years ago. From time to time this year fever. 3 days to feel dizzy, headache, with vague discourse, blurred vision of the right eye, right upper and lower limb activity is not working. Physical examination; anemia appearance, whole body skin and sclera yellow dye. Cardiopulmonary auscultation no abnormalities, liver and spleen is not. Pupil and other big. Vision: right nasal, left temporal irregular dark spots were defects. Slightly shallow right nasolabial fissure, the mouth a little skewed to the left, the tongue slightly to the right deviation, the amount of wrinkle closed eyes normal. Right upper and lower limb muscles