１概述遗传性肾炎又称Ａｌｐｏｒｔ综合征、家族性肾炎、遗传性进行性肾炎。１９世纪已有报道但未引起重视，至１９２７年Ａｌｐｏｒｔ进一步报道一个伴有神经性耳聋的家系后才受到普遍重视。发作性肉眼血尿伴进行性肾衰、神经性耳聋及眼晶状体病变为其特点。国内从１９７... 1 Overview Hereditary nephritis, also known as Alport syndrome, familial nephritis, hereditary progressive nephritis. Nineteenth century has been reported but did not pay attention, and by 1927 Alport further coverage of a family with nervous deafness received universal attention. Occurrence of gross hematuria with progressive renal failure, neurological deafness and eye lens disease as its characteristics. Domestic from 197 ...