腹膜后软组织肉瘤(retroperitoneal sarcoma,RPS)占所有软组织肉瘤的10%~15%,在美国其年发病率约为0.27/10万~([1-2]),目前无确切的关于中国患者的流行病学数据。迄今为止(至2016年1月),未发现该疾病的发病特征在不同的地区、人种及性别间存在显著的差异。从空间概念上,RPS系指原发于腹膜后间隙、不包括原发于腹膜后实质脏器如 Retroperitoneal sarcoma (RPS) accounts for 10% -15% of all soft tissue sarcomas, and its annual incidence in the United States is about 0.27 / 100000 ~ ([1-2]). There is no exact information about the Chinese patients Epidemiological data. To date (until January 2016), there was no significant difference in the incidence of the disease between different regions, ethnic groups and genders. From the concept of space, RPS refers to the primary retroperitoneal space, excluding the primary retroperitoneal organs such as