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真两性畸形罕见。我院三例经剖腹探查和病理检验得到证实,现报告如下。病例报告例一社会性别男,16岁,1979年12月第四次入院。患者自1976年(13岁)到1979年前后三次因尿道下裂来本院手术治疗。本次入院发现双乳房增大,而疑及两性畸形。检查:发育中等,皮下脂肪不多,声音似男性,但无胡须,喉结平。双侧乳房饱满,似少女乳房。阴毛稀少,阴茎短小、弯曲,尿道口位于根部腹侧。双侧阴囊被分开,两侧均有包块,左侧质地较柔软,右侧较硬略小,可摸到输精管条索。无阴道口,但于相应部位有皮肤凹陷。染色体检查为46XX,第二对不配对及断臂现象。染色质阴性。尿17-酮
Really rare genital hernia. Three cases of our hospital by laparotomy and pathological examination confirmed, are as follows. Case report, a gender male, 16 years old, in December 1979 the fourth admission. Patients from 1976 (13 years) to 1979 before and after three times due to hypospadias surgery in our hospital. The hospital found double breast enlargement, and suspicion of gender deformity. Check: medium development, small subcutaneous fat, sounds like a man, but no beard, Adam’s apple flat. Bilateral breast full, like a girl breasts. Sparse pubic hair, short penis, bending, urethra in the ventral root. Both sides of the scrotum are separated, both sides have mass, the left soft texture, the right hard slightly smaller, can touch the vas deferens cable. No vaginal mouth, but in the corresponding parts of the skin depression. Chromosomal examination 46XX, the second pair unpaired and broken arm phenomenon. Chromatin negative. Urine 17-ketone