先天性囊性腺瘤样畸形(congenital cystic adenomatoidmalformation,CCAM)是由异常发育的第三支气管所组成的肺发育畸形,这些支气管表现为错构瘤改变或停滞于胚胎发育期的各种大小的囊性病变,血液供应来源于肺循环,占先天性肺发育畸形的25%[1]。1949年Ch’in和Tang首先描述了CCAM病灶的病例特点[2],在此之前,CCAM与支气管肺隔离、先天性肺气肿、支气管源性囊肿和先天性支气管扩张等 Congenital cystic adenomatoid malformation (CCAM) is a developmental deformity of the lung that is composed of an abnormally developed third bronchus that exhibits cystic changes of all sizes or stagnation during embryonic development Lesions, blood supply from the pulmonary circulation, accounting for 25% of congenital lung dysplasia [1]. Ch’in and Tang first described the features of CCAM lesions in 1949 [2]. Prior to this, CCAM was isolated from bronchial lung, congenital emphysema, bronchogenic cyst and congenital bronchiectasis