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报告1例人体同种异体原位肝移植手术病例。受者为肝豆状核变性(腹型失代偿期),供者为男性脑死亡者。采用UW液灌注和保存,快速取肝。冷缺血时间为8小时。采用供体髂动脉架桥,重建变异肝动脉血供。术后应用环孢霉素合并泼尼松二联免疫抑制治疗,克服了腹腔迟发性大出血、急性排异反应、二重感染、霉菌感染及环孢霉素对肝脏的毒性作用等并发症。对术后出现的胆道并发症采用了经T管行胆道冲洗和Fogarty导管疏通于手术一年后胆道再通。目前受者已长期存活500天。
Report 1 case of human allogeneic orthotopic liver transplantation. Recipients of hepatolenticular degeneration (decompensated abdominal), donor for male brain death. UW fluid perfusion and preservation, rapid liver. Cold ischemia time is 8 hours. The donor iliac artery bridge was used to reconstruct the variant hepatic artery blood supply. Postoperative application of cyclosporine combined with prednisone divalent immunosuppressive therapy, to overcome the complications of delayed abdominal bleeding, acute rejection, double infection, fungal infection and cyclosporine toxicity on the liver and other complications. Biliary complications occurred after the use of the T-tube bile duct flushing and Fogarty catheter to clear the biliary recanalization after a year of surgery. The current recipient has long-term survival of 500 days.