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儿童颅咽管瘤的治疗仍有争议,本文总结了以显微外科手术行全切的50例病人.患者男28例,女22例.年龄1.8~17.6岁(平均9.39岁).症状有头痛、内分泌缺陷、视力障碍等.50例均行CT检查,均发现钙化,其它影像学表现有囊性变、蝶鞍扩大等.视交叉后肿瘤23例,其中有17例发生脑积水;视交叉前肿瘤25例,其中7例发生脑积水,两者间差异显著(P=0.005).手术主要取右额入路,并发症包括术中出血,癫痫、鼻出血等.结果:50例中有45例全切,5例次全切.1例术后死亡,3例失访,余46例随访期1~14年,平均4.86年.17例肿瘤复发,术后到复发的平均时间为
The treatment of pediatric craniopharyngioma is still controversial. This article summarizes the 50 patients who underwent microsurgery for total incision. The patients were 28 males and 22 females. Aged from 1.8 to 17.6 years (average 9.39 years). Symptoms of headache , Endocrine defects, visual impairment, etc. All 50 patients underwent CT examination and found to be calcified. Other imaging manifestations included cystic degeneration, sella enlargement, etc. 23 cases of tumors after optic chiasm, of which 17 cases developed hydrocephalus; Twenty-five tumors before crossover, of which 7 cases had hydrocephalus, there was a significant difference between the two (P=0.005). The operation mainly took the right frontal approach, complications included intraoperative bleeding, epilepsy, epistaxis, etc. Results: 50 cases Among them, 45 cases were all cut and 5 cases were totally cut. One case died after operation and 3 cases were lost to follow-up. The remaining 46 cases were followed up for 1 to 14 years with an average of 4.86 years. The tumors recurred in 17 cases. for