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本文报道3例患儿,并结合文献中的171例病例,对此病在儿童的临床表现、诊断和不同治疗方法进行了比较评价。由于此肿瘤可阻塞声门下气管,威胁生命,因此常需行气管切开术。文献报道的本病死亡率为19%。例1为6周女婴,有Sturge-Weber-Krabbe综合征,同时有进行性吸气性喘鸣。喉镜见喉室粘膜皱襞和声门下有血管瘤。行气管切开术。于17个月时拔管,无不良反应。例2为5个月女婴,出生时即有皮肤及粘膜
This article reports 3 cases of children, combined with 171 cases in the literature, the disease in children with clinical manifestations, diagnosis and different treatment methods were compared and evaluated. Because of this tumor can block the subglottic trachea, life-threatening, so often require tracheotomy. The reported mortality of the disease was 19%. Example 1 A 6-week-old baby with Sturge-Weber-Krabbe syndrome with progressive aspiration wheezing. Laryngeal see mucosal folds of the throat and vocal folds of hemangiomas. Tracheotomy. Extubation at 17 months, no adverse reactions. Case 2 is a 5-month-old baby girl with skin and mucous membranes at birth