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胃肠胰神经内分泌肿瘤(GEP-NENs)的发病率逐年增加,在这类肿瘤的诊治过程中,应充分重视多学科合作和建立区域诊治中心的重要性。改善生活质量、延长存活期和控制激素过量分泌的相关症状是神经内分泌肿瘤治疗的主要目标。这一领域仍有许多尚待解决的焦点问题,如准确的病理分级和分期、发现诊断和治疗的分子靶标、什么是适宜的治疗顺序和疗效评价手段、是否所有的神经内分泌瘤都需要治疗等,这些问题的解决有助于改善GEP-NENs的治疗效果。
The incidence of gastrointestinal pancreatic neuroendocrine tumors (GEP-NENs) is increasing year by year. In the diagnosis and treatment of such tumors, the importance of multidisciplinary cooperation and establishment of a regional diagnosis and treatment center should be given full attention. The main goals of neuroendocrine tumors are to improve the quality of life, prolong survival and control the associated symptoms of hormonal overdose. There are still many outstanding issues in this area, such as accurate pathological grading and staging, molecular targets for diagnosis and treatment, what is the appropriate treatment order and evaluation of efficacy, and whether all neuroendocrine tumors need treatment, etc. The resolution of these problems can help to improve the therapeutic effect of GEP-NENs.