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目的 :研究腮腺黏膜相关淋巴瘤 (Mucosa -AssociatedLymphoidTissueLymphoma ,MALToma)病理诊断特征及临床治疗。方法 :收集并分析临床资料 ,利用HE染色 ,LCA、CD2 0 、UCHL -1,κ链、λ链免疫组织化学标记观察 10例腮腺MALToma。结果 :腮腺MALToma组织学具有中心细胞样细胞弥漫浸润 ,浆细胞分化 ,淋巴滤泡破坏以及形成上皮 -肌上皮岛淋巴上皮病灶的特点。免疫组化证实其来源为B细胞淋巴瘤。结论 :①本组 11例原发腮腺恶性淋巴瘤均属于MALToma。②部分 (3 6% )伴良性淋巴上皮病及舍格林综合症提示 ,本组MALToma可能与自身免疫性疾病有关。③手术切除辅以适当化疗可获较好疗效。
Objective: To study the pathological diagnosis and clinical treatment of mucosa-associated lymphoma Tissue Lymphoma (MALT). Methods: Clinical data were collected and analyzed. Ten cases of parotid gland MALToma were observed by HE staining, LCA, CD20, UCHL -1, κ chain and λ chain immunohistochemical staining. Results: Parotid MALToma histology had diffuse infiltration of central cell-like cells, differentiation of plasma cells, destruction of lymphatic follicles and formation of epithelial-myofibular island lymphoepithelial lesions. Immunohistochemistry confirmed its origin as B cell lymphoma. Conclusions: ① The 11 primary parotid malignant lymphoma belong to MALToma. ② part (36%) with benign lymphoepithelial and Sjogren’s syndrome suggest that this group of MALToma may be related to autoimmune diseases. ③ surgical resection supplemented by appropriate chemotherapy can be a better effect.