纤毛黏液结节性乳头状肿瘤是一种罕见的肺外周病变,以乳头状结构和纤毛柱状细胞与黏液细胞、基底细胞混合为特征。常出现显著的肺泡腔内黏液,可能导致与黏液腺癌诊断上的混淆。诊断纤毛黏液结节性乳头状肿瘤的关键在于对具有纤毛柱状细胞的识别。目前文献报道较少,且均发生于东亚患者。尽管随访资料有限,但是纤毛黏液结节性乳头状肿瘤属于惰性肿瘤,预后较好。因此有学者质疑其是否为一种反应性或错构瘤性 Ciliated mucinous nodular papillary tumor is a rare peripheral lung disease characterized by papillary structures and ciliated columnar cells mixed with mucus cells and basal cells. Often significant alveolar mucus appears and may lead to confusion with the diagnosis of mucinous adenocarcinoma. The key to diagnosis of ciliated mucinous papillary tumors is the identification of ciliated cells. At present, there are few reports in the literature, and all occurred in East Asian patients. Despite limited information on follow-up, ciliated mucinous nodular papillary neoplasms are inactive tumors with good prognosis. Therefore, some scholars question whether it is a reactive or hamartoma