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恶性网状细胞增多症(或称恶性组织细胞增多症,下简称恶网)是原发于网状内皮系统的恶性疾病,其特点是异常网状细胞呈肿瘤样增生,伴有对红细胞、淋巴细胞及血小板的吞噬现象;病变可累及全身,病程凶险短促,预后极差。临床诊断十分困难,特别是原发于内脏的病例,易致误诊,有的直至尸解时始被证实。随着对本症认识的不断提高和细胞形态学研究的逐步进展,本病报导逐年增加。
Malignant reticulocytosis (or malignant histiocytosis, hereinafter referred to as evil nets) is a malignant disease originating in the reticuloendothelial system, which is characterized by abnormal reticular cells were tumor-like hyperplasia, accompanied by erythrocytes, lymph Cells and platelets phagocytosis; lesions can affect the whole body, the course of dangerous short-term, poor prognosis. Clinical diagnosis is very difficult, especially in the cases of internal organs, easily lead to misdiagnosis, and some confirmed until the autopsy. With the continuous improvement of awareness of the disease and the gradual progress of cell morphology research, the incidence of this disease increased year by year.