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血栓性血小板减少性紫癜(TTP)与溶血性尿毒性综合征(HUS)属微血管病性溶血性贫血(MHA)范畴内的疾病。所谓MHA是指在微血管病变的基础上,由于机械性因素使红细胞在微血管内碎裂,导致溶血性贫血,血象中出现盔形、棘形、三角形、微小球形、碎片和其他畸形红细胞是其特点,并常伴有血小板减少所致的出血现象。
Thrombotic thrombocytopenic purpura (TTP) and hemolytic uremic syndrome (HUS) are microvascular disease hemolytic anemia (MHA) category of disease. The so-called MHA is based on the microvascular lesions, due to mechanical factors in the red blood cells within the fragmentation of the capillaries, leading to hemolytic anemia, blood appeared helmet-shaped, spine-shaped, triangular, spherical, debris and other abnormal red blood cells is its characteristics , And often accompanied by thrombocytopenia bleeding.