毛细血管性血管母细胞瘤是组织起源未定的WHO分类Ⅰ级的肿瘤 ,是由基质细胞和丰富的毛细血管组成。5 %～38 %的中枢神经系统毛细血管性血管母细胞瘤与vonHippel-Lindau病有关。毛细血管性血管母细胞瘤大多发生在小脑 ,无论肿瘤发生在小脑、脑干和大脑半球 ,都有相似的CT、MRI表现。瘤体常有囊性区和实质性壁结节 ,增强扫描壁结节有强化 ,而囊壁则可有或无强化。部分毛细血管性血管母细胞瘤表现为实质性肿块 ,增强时伴有强化 ,实质性者通常较小 Capillary angioblastoma is a WHO class I tumor of undetermined origin of tissue consisting of stromal cells and abundant capillaries. 5% to 38% of central nervous system capillary hemangioblastoma and vonHippel-Lindau disease. Capillary hemangioblastoma mostly occurs in the cerebellum and has similar CT and MRI findings regardless of whether the tumor occurs in the cerebellum, brain stem or hemisphere. Tumor often cystic area and substantial wall nodules, enhanced scan nodules have enhanced, while the wall may or may not have enhanced. Some of the capillary hemangioblastoma manifested as a substantial mass, enhanced with enhancement, the substance is usually smaller