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肺泡蛋白沉积症(pul monary alveolar proteinosis,PAP)是指磷脂蛋白样物质在肺泡腔内积聚所导致的一种罕见疾病。虽然近年来有报道外源性粒细胞-巨噬细胞集落刺激因子(Granulocyte-macrophage colony-sti mulating factor,GM-CSF)和经纤维支气管镜分段肺灌洗治疗PAP取得了一定
Pulmonary alveolar proteinosis (PAP) is a rare disease caused by accumulation of phospholipid-like substances in the alveolar space. Although it has been reported in recent years that exogenous granulocyte-macrophage colony-stimulating factor (GM-CSF) and pulmonary bronchofocalconeal lavage treated with PAP have achieved certain