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孕妇,28岁。孕1产0,否认孕期前后有不良环境接触史、家族遗传史。孕26周胎儿常规超声检查:胎儿发育和孕周相符。胎儿心脏超声检查:胎儿右房、右室增大,三血管切面显示升主动脉细窄,笔直向上,发出头臂干动脉及左颈总动脉,未形成主动脉弓;左锁骨下动脉起自降主动脉(图1)。肺动脉内径明显增宽,动脉导管异常粗大。室间隔上断回声中断,最大间距0.46 cm。彩色多普勒显示:室间隔上段探及双向分流信号。超声提示:宫内单活胎;胎儿
Pregnant woman, 28 years old. Pregnancy 1 0, denied before and after pregnancy have adverse environmental exposure history, family history. 26 weeks pregnant fetus conventional ultrasound: fetal development and gestational age line. Fetal heart ultrasound: Fetal right atrium, right ventricular enlargement, three blood vessels showed a narrow ascending aortic stenosis, straight up, issued a brachiocephalic and left common carotid artery, did not form aortic arch; left subclavian artery from the main Artery (Figure 1). Pulmonary artery diameter was significantly widened, abnormal ductus arteriosus. Interrupted septal echo was interrupted, the maximum spacing of 0.46 cm. Color Doppler display: Septal exploration and bidirectional shunt signal. Ultrasound Tip: intrauterine single live fetus; fetus