作者报告了最近遇到的一个家族中至少有四个成员患肝细胞腺瘤,受累的家庭成员都患糖尿病。两侧有卵巢硬化。两个祖先死于肝细胞瘤。这个不常见的伴有内分泌异常的家族,可能给这些罕见的肝脏损害原因提供线索。作者对这个家庭作了家系调查,四代二十人中有十二人患糖尿病。表明这个家庭中的高度外显率。受累的四例均有正常的性发 The authors reported that at least four members of a recently encountered family had hepatocellular adenomas and affected family members had diabetes. Ovarian sclerosis on both sides. Two ancestors died of hepatoma. This unusual family with endocrine abnormalities may provide clues to these rare causes of liver damage. The authors conducted a family survey of the family, and 12 out of four people in the four generations had diabetes. Indicates the high penetrance in this family. The four affected patients had normal hair