恶性纤维组织细胞瘤(MFH)绝大部分都发生于软组织,原发于骨者少见。近年来由于组织培养、组织化学和电镜等先进技术的应用,原发于骨的恶性纤维组织细胞瘤才逐渐为人们所认识。自1974年Spanier等明确提出骨的原发性恶性纤维组织瘤的诊断后,在国外陆续有报告,国内 The vast majority of malignant fibrous histiocytoma (MFH) occurs in soft tissues and is rare in primary bones. In recent years, due to the application of advanced techniques such as tissue culture, histochemistry, and electron microscopy, malignant fibrous histiocytoma, originally found in bone, has gradually become known. Since the diagnosis of primary malignant fibrous tissue tumors of bone was clearly proposed by Spanier et al. in 1974, there have been successive reports in foreign countries.