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目的:分析颅内血管网状细胞瘤的临床特点。方法:对我院1975年~1996年收治并经病理证实的血管网状细胞瘤38例作一回顾性研究。结果:发病年龄多数为20~50岁,男性多于女性,绝大多数发生于小脑。26例行CT检查,肿瘤分囊性者23例,其中4例又作MRI检查,肿瘤为囊性者3例。瘤结节及实性肿瘤全切除36例,部分切除加放射治疗2例。结论:MRI检查对囊性血管网状细胞瘤的诊断有特异性;手术切除程度和病变呈多灶性与肿瘤复发有关;肿瘤具有明显的遗传倾向。
Objective: To analyze the clinical features of intracranial vascular reticular tumor. Methods: A retrospective study was performed on 38 patients with vascular reticular neoplasia who were admitted to our hospital from 1975 to 1996 and confirmed by pathology. Results: The majority of onset age was 20 to 50 years old, more men than women, the vast majority occurred in the cerebellum. Twenty-six patients underwent CT examination. Twenty-three patients were divided into two groups, of which four were MRI and three were cystic. Tumor nodules and solid tumors in 36 cases of total resection, partial excision plus radiation therapy in 2 cases. Conclusion: The MRI examination is specific for the diagnosis of cystic vascular reticular cell tumor. The degree of resection and the multifocal lesion are related to tumor recurrence. The tumor has obvious genetic predisposition.