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1984年~1991年该科共收治颅底颈椎脊索病12例,其中颅底10例,颈椎2例。男性8例。全组平均年龄38.7岁。所有病例均行术后60Co放射治疗,颅底、颈椎平均剂量分别是52.2Gy/5.5周和40Gy/4~5周。4例行肉眼肿瘤全部切除术,6例行肿瘤不全切除术,2例行活检减压术。5、10年生存率分别是41.6%和28.5%。9例治疗后复发(75%),3例伴远处转移。复发是治疗失败的关键。远处转移少见,但存在远期的转移和复发,所以应长期随访。彻底的手术加本后放射治疗是最佳治疗手段。三维立体定向治疗计划系统指导的带电粒子(质子及氦氖离子)放射治疗已改善了该病的预后。
From 1984 to 1991, the department received a total of 12 cases of cervical chordate prominence, including 10 cases of skull base and 2 cases of cervical spine. 8 males. The average age of the group was 38.7 years old. All patients underwent 60Co radiotherapy after operation. The average skull base and cervical vertebrae were 52.2 Gy / 5.5 weeks and 40 Gy / 4 ~ 5 weeks respectively. 4 cases of total resection of gross tumor, 6 cases of tumor resection, 2 cases of biopsy decompression. The 5-year and 10-year survival rates were 41.6% and 28.5% respectively. Nine patients relapsed after treatment (75%) and three had distant metastases. Recurrence is the key to failure of treatment. Remote metastasis rare, but there is a long-term metastasis and recurrence, it should be long-term follow-up. Thorough surgery plus radiotherapy is the best treatment. Three-dimensional stereotactic treatment planning system directed charged particles (proton and helium-neon) radiation therapy has improved the prognosis of the disease.