青年人猝死多与肥厚性心肌病、二尖瓣脱垂和心脏传导系统异常有关.作者通过对大量猝死年轻人的尸检,意外地发现右室心肌病是造成青年人猝死更为常见的病因.方法:患者为1979—1986年意大利威尔斯地区登记的,年龄<35岁的猝死病人,由 Padua 大学病理解剖研究所进行细致的心脏形态学检查,包括心脏重量、室壁厚度的测量,冠状动脉和瓣膜的检查,心室游离壁和室间隔心肌的组织学检查以及传导系统的组织学检查.结果:60例猝死病人,男39,女21,年龄1.5—35岁(平均22.3岁).心源性猝死56例(93%),其中冠状动脉病变19例,右室心肌病12例,传导系统异常12例,主动脉破裂5例,肥厚心肌病3例,二 Sudden death among young people is mostly associated with hypertrophic cardiomyopathy, mitral valve prolapse and abnormal cardiac conduction system.The authors unexpectedly found that right ventricular cardiomyopathy is the more common cause of sudden death in young people through an autopsy of a large number of sudden death young adults. METHODS: Patients were sudden-onset patients <35 years of age registered in the Welsh Region of Italy from 1979 to 1986 and meticulous cardiac morphological examination by the Institute of Pathology and Anatomy, Padua University, including measurement of heart weight, wall thickness, coronal Arterial and valvular examination, histological examination of ventricular free wall and interventricular septal myocardium, and histological examination of the conduction system.Results: Sixty sudden cases of death, male 39, female 21, aged 1.5-35 years (average 22.3 years) Sudden death in 56 cases (93%), of which 19 cases of coronary lesions, 12 cases of right ventricular cardiomyopathy, conduction system abnormalities in 12 cases, 5 cases of aortic rupture, hypertrophic cardiomyopathy in 3 cases,