先天性一侧肾缺如,较为少见,过去多在尸体解剖中发现。自X线及肾盂造影剂相继发明后,有关这种疾病的国内外文献报导逐渐增加。国内施谢二氏于1936年曾报告二例。李魏二氏报告三例。但本文所报告先天性右侧孤立肾,109块肾结石,并发巨大型肾盂积水,国内尚未见报导。病例报告患者牛××,男性,25岁,住院号19976,1958年5月5日以主诉五天来阵发性腹痛,及无尿,右腹部突然生一肿物。现在史:患者于58年4月30日,正在重体力劳动时,突然感觉 Congenital kidney deficiency, the more common, the past more than found in the autopsy. Since the X-ray and pyelography have been invented one after another, the domestic and foreign literature on the disease is gradually increasing. Domestic Xie Xie Er had reported two cases in 1936. Li Wei’s report of three cases. However, this report reports the congenital isolated right kidney, 109 kidney stones, massive hydronephrosis, has not been reported in China. Case Report Niu × ×, male, 25 years old, hospital number 19976, May 5, 1958 to complain five days to paroxysmal abdominal pain, and anuria, abdomen suddenly gave birth to a mass. Now history: the patient on April 30, 58, is heavy manual labor, suddenly felt