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报告一例男性6岁患儿,主诉生后鼻翼发育不全和呼吸困难。体检:外鼻畸形:鼻中隔右偏;左鼻腔前份可见一粉红色、广基、硬性肿物,起自中隔。于气管插管麻醉下摘除肿瘤。标本呈圆形、质硬,直径约1.5cm。组织学检查:肿瘤由圆形及卵圆形的星形细胞组成,胞浆突起不明显,核圆形,核染色质呈细腻网状结构,细胞间充满胶原纤维。诊断:神经胶质瘤。作者指出:本病属罕见良性肿瘤,1900年Schmidt首次报道,迄今世界文献中仅报道60
A case of a 6-year-old male patient was reported complaining of dysplasia and dyspnea after birth. Physical examination: external nasal deformity: right septum; the left nasal cavity can be seen in front of a pink, broad-based, rigid tumor, from the septum. The tumor was removed under tracheal intubation anesthesia. Specimens are round, hard and about 1.5cm in diameter. Histological examination: The tumor consisted of round and oval stellate cells. The cytoplasmic projections were not obvious. The nucleus was round and the nuclear chromatin was fine and reticular. The cells were filled with collagen fibers. Diagnosis: glioma. The authors pointed out that this disease is a rare benign tumor. It was first reported by Schmidt in 1900. So far only 60 reports have been reported in the world literature.