Pendred 氏综合征是一种先天性聋哑并有甲状腺肿的综合征。据国外统计本病占聋哑人的1%,占先天性聋哑人的2～10%,在英国有10%的儿童患有此病,在我国尚未见到该病的统计材料。尽管该病在甲状腺门诊或耳鼻喉科门诊适可见到,但易被临床医师所忽视,现将我们遇到的两例先天性聋哑伴有甲状腺肿综合征 Pendred 氏综合征报告如下: Pendred’s syndrome is a congenital deaf and dull goiter syndrome. According to foreign statistics, the disease accounts for 1% of the deaf-mutes and accounts for 2% to 10% of the deaf-mutes. In the United Kingdom, 10% of the children suffer from this disease and no statistical material has been found in our country. Although the disease can be seen in thyroid clinic or otolaryngology clinic, but easily overlooked by clinicians, now we encounter two cases of congenital deafness associated with goiter syndrome Peeth’s syndrome are reported as follows: