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淋巴结内栅栏状肌纤维母细胞瘤是一种良性的、发病机制未明的肌纤维母细胞性肿瘤。作者报道一组有关这种罕见肿瘤的临床病理、免疫组化及分子遗传学特征。本组病例中14例男性,4例女性;年龄范围31~65岁,平均年龄47岁,中位年龄49岁;肿瘤位于腹股沟淋巴结15例,颈部淋巴结1例,未知部位淋巴结2例。多数患者表现为无痛性肿块或结节,4例有腹股沟区可能的外伤史。瘤体直径1~4.2 cm,平均3.1 cm,中位3 cm。镜下肿瘤边界清楚,多为假包膜性结节(n=17)或真性结
Fetal myofibroblastic tumor in the lymph nodes is a benign, myofibroblastic tumor of unknown pathogenesis. The authors report a group of clinicopathological, immunohistochemical and molecular genetic features related to this rare tumor. The group of patients 14 males and 4 females; age range of 31 to 65 years, mean age 47 years, median age 49 years; tumor located in the inguinal lymph node in 15 cases, 1 case of cervical lymph nodes, unknown part of the lymph nodes in 2 cases. The majority of patients showed painless mass or nodules, and 4 patients had a history of possible trauma in the inguinal region. Tumor diameter 1 ~ 4.2 cm, an average of 3.1 cm, the median 3 cm. Microscopic tumor border clear, mostly pseudocapillary nodules (n = 17) or true sex knot