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婴儿期维生素 K 依赖因子缺乏症又称婴儿自然出血症或叫婴儿出血综合症。以往认为本病仅发生于新生儿期,尤其是初生2~3天。近年来发现婴儿期出现的与新生儿出血症相似的一种出血性疾病临床并不少见。尤其可有严重的出血性现象甚至颅内出血。姚×,男,50天。系第二胎足月顺产。生后一般情况好,因乳喂养。母孕期健康,家族史无特殊。因患“支气管肺炎并腹泻”在当地肌注青霉素时出现扎针处出血不止,并发现全身有散在暗紫色瘢块,有的呈硬结状。发病第三天患儿高烧39℃,抽搐,抽搐缓解后但扎针处出血不止。急来我院,立即作血液化验,耳垂采血处出血不止。体检:急性病容,面色苍白,呼吸急促。全身多处
Infant vitamin K-dependent deficiency, also known as infantile hemorrhagic disease or called infant hemorrhagic syndrome. In the past that the disease occurs only in the neonatal period, especially the newborn 2 to 3 days. In recent years, it has been not uncommon to find a hemorrhagic disease similar to that of neonatal hemorrhage in infancy. In particular, there may be severe hemorrhagic or intracranial hemorrhage. Yao ×, male, 50 days. Department of second-term full-term birth. After birth, the general situation is good, because of breast feeding. Pregnant during pregnancy, family history no special. Because of suffering from “bronchial pneumonia and diarrhea,” when there is bleeding in the local muscle penicillin syphilis bleeding, and found that the whole body scattered in the dark purple scar, and some were hardened. The third day of onset of children with fever 39 ℃, convulsions, convulsions ease but after the needle at bleeding more than. Emergency to our hospital, immediately for blood tests, bleeding ear lobe bleeding more than. Physical examination: acute disease, pale, shortness of breath. Multiple body