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目的 探讨僵肢综合征 (SLS)临床及电生理特点。方法 对 1例僵肢综合征临床资料进行分析 ,并综合文献 ,阐述该病的临床及电生理特点、治疗方法及预后。结果 僵肢综合征是僵人综合征的变异型的一种 ,多与自身免疫及副肿瘤性两种因素有关 ,肌电图显示在静息时出现连续运动单位活动 (CMUA)。与经典僵人综合征 (SMS)不同 ,多表现为肢体远端强直及痛性痉挛 ,躯干相对较少累及 ;患者有多种抗体 ,糖尿病及血清抗谷氨酸脱羧酶抗体 (GAD)较少见 ,个别患者患乳腺癌或肺小细胞癌 ;治疗效果不如经典SMS。结论 这是 1例罕见的乳腺癌伴僵肢综合征的病例 ,根据临床特点、肌电图可以确诊 ,具有副肿瘤性及免疫学异常的特点 ,切除肿瘤后用大剂量激素及安定类药物治疗有效。
Objective To investigate the clinical and electrophysiological characteristics of stiff limb syndrome (SLS). Methods The clinical data of one case of stiff limb syndrome were analyzed, and the clinical and electrophysiological characteristics, treatment and prognosis of the disease were summarized. Results The limb-flexural syndrome was a variant of stiff-person syndrome, which was mainly related to autoimmunity and paraneoplasticity. Electromyography showed continuous motor activity (CMUA) at rest. Unlike the classic stiff human syndrome (SMS), which is characterized by distal rigidity and painful cramping, the torso is relatively infrequent; patients have a variety of antibodies, and diabetes and serum anti-glutamic acid decarboxylase antibody (GAD) See, individual patients with breast cancer or small cell lung cancer; treatment is not as good as the classic SMS. Conclusion This is a rare case of breast cancer with stiff limb syndrome. According to the clinical features, EMG can be diagnosed with the characteristics of paraneoplastic and immunological abnormalities. After removal of the tumor, high dose hormones and tranquillizers effective.