论文部分内容阅读
神经节神经胶质瘤(Ganglioglioma)占脊髓肿瘤的1.1%,而脊髓园锥神经节神经胶质瘤在文献中尚未见报导。本文报告一例成功摘除后经组织学证实的园锥脊髓内神经节神经胶质瘤。患儿男性、2岁半,系正常妊娠和分娩,一岁时出现步态失调呈鸽步(Pigeonlike),入院前两周加重并有括约肌功能障碍,而于1983年3月2日入院。检查:步行时双踝外翻,双下肢肌无力,以近端为重,肌张力和腱反射均减低,左侧Babinski(十)。右侧T_(12)水平以下有感觉障碍。脊椎X线照片显示T_(10)～L_2椎管增宽,经腰部和C_(1-2)侧方穿刺行脊髓腔造影检查,椎管内梗阻显示为硬膜内髓内病变,病变位于L_2-T_(10)。将T_(10)-L_2椎板切除经探查证实为髓内肿瘤,肿瘤囊壁较厚、富于血管,在显微手术下行肿瘤切除,组织学检查证实为神经节神经胶质瘤。术后近端肌力逐渐恢复,15个月后恢复正常。
Ganglioglioma accounts for 1.1% of spinal cord tumors, and no report of spinal cord conus ganglion glioma has been reported in the literature. This article reports a case of successful removal of the conusial spinal cord ganglion glioma confirmed by histology. The children were male, 2 and a half years old. They were normal pregnancy and childbirth. At the age of one year, the gait disorder was Pigeonlike. He was aggravated two weeks before admission and had sphincter dysfunction. He was admitted to hospital on March 2, 1983. Examination: When both legs are valgus during walking, the muscles of both lower limbs are weak, and the proximal end is the most important. Muscle tension and tendon reflexes are reduced, left Babinski (10). There is a sensory disturbance below the right T_(12) level. X-ray photographs of the spine show that the T_(10)~L_2 spinal canal is widened and spinal cord angiography is performed through the lumbar and C_(1-2) lateral puncture. Intraspinal obstruction is shown as an intradural intramedullary lesion, and the lesion is located at L_2 -T_(10). The T_(10)-L_2 laminectomy was proved to be an intramedullary tumor. The tumor wall was thick and rich in blood vessels. The tumor was removed under microsurgery. Histologic examination confirmed ganglional glioma. The proximal muscle strength gradually recovered after surgery and returned to normal after 15 months.